Cystic renal lymphangiectasia: A distinctive clinicopathologic entity in the pediatric age group

Susan C. Simonton, Daniel A. Saltzman, William Brennom, Michael Pergament, Gordon Drake, Alan Sinaiko, John R. Priest

Research output: Contribution to journalArticlepeer-review

Abstract

This report describes the features of unilateral cystic renal lymphangiectasia in a 2-year-old child who presented with hypertension, massive ascites, a left flank mass, and no evidence of familial renal cystic disease. The child became normotensive and is now asymptomatic more than 3 years after surgery. The clinical presentation and diffuse pathologic involvement are similar to findings for the few pediatric patients with cystic lymphangiectasia described in the literature and appear distinct from the more localized form of the disease seen in adults.

Original languageEnglish (US)
Pages (from-to)293-301
Number of pages9
JournalFetal and Pediatric Pathology
Volume17
Issue number2
DOIs
StatePublished - Dec 1 1997

Keywords

  • cystic renal disease
  • parapelvic cysts
  • renal lymphangiectasia
  • renal lymphangioma

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