TY - JOUR
T1 - Papillary intralymphatic angioendothelioma of the thigh
T2 - A case report and review of the literature
AU - Ward, Katherine A.
AU - Ecker, Phillip M.
AU - White, Rebekah R.
AU - Melnik, Tanya E.
AU - Gulbahce, Evin H.
AU - Wilke, Mark S.
AU - Sangueza, Omar P.
PY - 2010/4
Y1 - 2010/4
N2 - The term angiosarcoma, encompasses several neoplasms, all of which exhibit a malignant process derived from endothelial cells of the vessels. The most common form of angiosarcoma is highly aggressive, often fatal, and usually affects the head and neck region of elderly white men. Other low-grade forms of angiosarcoma, including papillary intralymphatic angioendothelioma, also known as Dabska tumor, are less invasive, affect a wider age range, and offer a better prognosis. There are several predisposing factors that increase the risk of angiosarcoma and include chronic lymphedema of the extremities, preexisting vascular lesions, and prior radiation, often as therapy for other malignancies. We report an unusual case of a very small, low-grade angiosarcoma on the thigh of an adult female with no known predisposing risk factors.
AB - The term angiosarcoma, encompasses several neoplasms, all of which exhibit a malignant process derived from endothelial cells of the vessels. The most common form of angiosarcoma is highly aggressive, often fatal, and usually affects the head and neck region of elderly white men. Other low-grade forms of angiosarcoma, including papillary intralymphatic angioendothelioma, also known as Dabska tumor, are less invasive, affect a wider age range, and offer a better prognosis. There are several predisposing factors that increase the risk of angiosarcoma and include chronic lymphedema of the extremities, preexisting vascular lesions, and prior radiation, often as therapy for other malignancies. We report an unusual case of a very small, low-grade angiosarcoma on the thigh of an adult female with no known predisposing risk factors.
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M3 - Article
C2 - 20409411
AN - SCOPUS:77953097324
SN - 1087-2108
VL - 16
JO - Dermatology Online Journal
JF - Dermatology Online Journal
IS - 4
ER -