Abstract
Pulmonary artery angiosarcoma is a rare malignant vascular tumor with an aggressive clinical course and a poor prognosis. Hemoptysis and shortness of breath have been reported as common clinical presentations. The exact clinicopathology is unknown. A tissue specimen obtained by percutaneous fine-needle aspiration cytology or open/thoracoscopic biopsy can confirm the diagnosis based on histopathological and immunohistochemical features. The differential diagnosis includes pulmonary thromboembolism, vascular malformations, and lung carcinoma. There is a paucity of literature describing this tumor, with only a few case reports available. There is also a lack of standardized guidelines for management, which further worsens the survival outcome. We report 3 cases of pulmonary artery angiosarcoma and review the recent literature.
Original language | English (US) |
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Pages (from-to) | 347-352 |
Number of pages | 6 |
Journal | Asian Cardiovascular and Thoracic Annals |
Volume | 27 |
Issue number | 5 |
DOIs | |
State | Published - Jun 1 2019 |
Externally published | Yes |
Keywords
- Diagnosis
- differential
- hemangiosarcoma
- immunohistochemistry
- mediastinal neoplasms
- pulmonary artery
- vascular neoplasms
PubMed: MeSH publication types
- Case Reports
- Journal Article
- Review