TY - JOUR
T1 - Ross-Konno and endocardial fibroelastosis resection after hybrid stage i palliation in infancy
T2 - Successful staged left-ventricular rehabilitation and conversion to biventricular circulation after fetal diagnosis of aortic stenosis
AU - Moon-Grady, Anita J.
AU - Moore, Phillip
AU - Azakie, Anthony
PY - 2011/2
Y1 - 2011/2
N2 - We report a patient who presented during fetal life with severe aortic stenosis, left-ventricular dysfunction, and endocardial fibroelastosis (evolving hypoplastic left heart syndrome). Management involved in utero and postnatal balloon aortic valvuloplasty for partial relief of obstruction and early postnatal hybrid stage I palliation until recovery of left-ventricular systolic function had occurred. The infant subsequently had successful conversion to a biventricular circulation by combining resection of endocardial fibroelastosis with single-stage Ross-Konno, aortic arch reconstruction, hybrid takedown, and pulmonary artery reconstruction.
AB - We report a patient who presented during fetal life with severe aortic stenosis, left-ventricular dysfunction, and endocardial fibroelastosis (evolving hypoplastic left heart syndrome). Management involved in utero and postnatal balloon aortic valvuloplasty for partial relief of obstruction and early postnatal hybrid stage I palliation until recovery of left-ventricular systolic function had occurred. The infant subsequently had successful conversion to a biventricular circulation by combining resection of endocardial fibroelastosis with single-stage Ross-Konno, aortic arch reconstruction, hybrid takedown, and pulmonary artery reconstruction.
KW - Aortic stenosis
KW - Fetal balloon aortic valvuloplasty
KW - Fetal intervention
KW - Hypoplastic left heart syndrome
KW - Resection of endocardial fibroelastosis
KW - Stage 1 hybrid
UR - http://www.scopus.com/inward/record.url?scp=79952313200&partnerID=8YFLogxK
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U2 - 10.1007/s00246-010-9841-3
DO - 10.1007/s00246-010-9841-3
M3 - Article
C2 - 21107553
AN - SCOPUS:79952313200
SN - 0172-0643
VL - 32
SP - 211
EP - 214
JO - Pediatric Cardiology
JF - Pediatric Cardiology
IS - 2
ER -