Purpose: To assess the efficacy of goniotomy/trabeculotomy as the initial surgical procedure in early-onset glaucoma associated with Sturge-Weber syndrome. Methods: We retrospectively analyzed 16 eyes of 14 consecutive patients with Sturge-Weber syndrome-associated glaucoma diagnosed before 4 years of age. All subjects were seen at a single institution from 1978 to 1996 and underwent goniotomy or trabeculotomy as their initial surgical procedure. Results: Twelve eyes underwent initial goniotomy, and 4 eyes underwent initial trabeculotomy. One subject was lost to follow-up after surgery, resulting in 15 eyes for analysis. Of the initial goniotomy eyes, two thirds required a second surgical procedure. In the initial trabeculotomy eyes, half required a second procedure. Intraocular pressure was controlled (intraocular pressure ≤22 mm Hg) in 66.7% of the eyes (10 of 15) after one or more goniotomy or trabeculotomy procedures for a median follow-up of 5.4 years (range, 1.4 to 15 years). For eyes with only one surgical procedure, 4 of 6 eyes had controlled intraocular pressure over a median follow-up of 3.4 years (range, 3 to 12 years). Seven of the 9 eyes that required more than one procedure had controlled intraocular pressure after all procedures over a median follow-up of 4.5 years (range, 1.4 to 15 years). Conclusion: Initial or repeated goniotomy or trabeculotomy may be an effective management choice for treatment of glaucoma associated with Sturge-Weber syndrome presenting in early childhood.
Bibliographical noteFunding Information:
From the Department of Ophthahnology, University of Minnesota, Minneapolis, Minnesota, Supported by an unrestrictedg rant from the Research to Prevent Blindness Foundation. Submitted February Y, 1998. Revision acceptedA ugust 12; 1998. Reprint requests: Agnes S. Huang, MD, Box 495 FUMHC, 420 Delaware St SE, Minneapolis, MN YY 4Y Y -OYO1. Copyright © 1998 by the American Association for Pediatric Ophthalmology and Strabismus. 1091-8Y31/98 $5.00 + 0 75/1/95096
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