Aortic stenosis in a patient with Hurler's syndrome after bone marrow transplantation

Naruhito Watanabe; Petros V. Anagnostopoulos; Anthony Azakie

doi:10.1017/S1047951110002015

Aortic stenosis in a patient with Hurler's syndrome after bone marrow transplantation

Naruhito Watanabe, Petros V. Anagnostopoulos, Anthony Azakie

Surgery

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Abstract

We describe a case of severe aortic stenosis in a 16-year-old male with Hurler's syndrome who had prior bone marrow transplantation. The excised aortic valve leaflets showed characteristic pathologic findings of Hurler's syndrome. This is the first case report of aortic valve replacement in a patient with Hurler's syndrome treated with bone marrow transplantation that demonstrates progression of the aortic valve disease despite treatment.

Original language	English (US)
Pages (from-to)	349-350
Number of pages	2
Journal	Cardiology in the young
Volume	21
Issue number	3
DOIs	https://doi.org/10.1017/S1047951110002015
State	Published - Jun 2011

Keywords

Mucopolysaccharidosis
aortic valve replacement
valvular disease

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This output contributes to the following UN Sustainable Development Goals (SDGs)

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KW - valvular disease

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Aortic stenosis in a patient with Hurler's syndrome after bone marrow transplantation

Abstract

Keywords

UN SDGs

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